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. Author manuscript; available in PMC: 2024 Jan 1.
Published in final edited form as: Birth Defects Res. 2022 Jun 6;115(1):56–66. doi: 10.1002/bdr2.2050

TABLE 3.

Associations between pregestational type 1 and type 2 diabetes and cardiac birth defects included in the National Birth Defects Prevention Study, 1997–2011

No diabetes
Pregestational type 1 diabetes
Pregestational type 2 diabetes
All
All
All
Birth defect Unexposeda Type 1
exposeda
Type 1 OR
(95% CI)b
Type 2
exposeda
Type 2 OR
(95% CI)b
Heterotaxy 307 9 13.5 (5.7, 29.3) 11 11.8 (5.4, 24.1)
Conotruncal defects
  Truncus arteriosus 114 3 11.9 (2.3, 39.9) 9 20.3 (8.7, 44.0)
  Tetralogy of Fallot 1,060 8 3.7 (1.6, 7.9) 20 5.1 (2.8, 9.1)
  d-TGA 708 9 5.5 (2. 5, 11.4) 4 1.8 (0.5, 5.1)
  DORV-TGA 174 5 10.8 (3.4, 27.6) 3 5.5 (1.1, 17.7)
  Conoventricular septal Defectc,d 102 0 NC 6 22.6 (7.7, 60.5)
   Atrioventricular septal defect 324 7 9.4 (3.8, 20.7) 10 12.5 (5.7, 25.2)
   TAPVR 272 2 NC 3 3.5 (0.7, 11.3)
LVOTO defects
  HLHS 579 1 NC 9 4.9 (2.1, 10.3)
  Coarctation of the aorta 1,047 8 3.4 (1.4, 7.3) 16 5.4 (2.9, 9.8)
  Aortic stenosis 467 4 3.9 (1.0, 11.3) 8 5.8 (2.4, 12.7)
RVOTO defects
  Pulmonary atresia 240 0 NC 6 6.0 (2.1, 14.2)
  Pulmonary valve stenosisc,d 1,389 12 3.8 (1.8, 7.8) 16 3.6 (1.9, 6.6)
  Tricuspid atresia 160 2 NC 4 8.0 (2.0, 22.7)
   Ebstein anomaly 171 0 NC 1 NC
Septal defects
  Perimembranous VSDc,d 1,313 14 4.6 (2.1, 10.2) 24 5.7 (3.0, 11.0)
  Muscular VSD 176 0 NC 1 NC
  Secundum or ASD NOS 2,680 45 7.4 (4.4, 12.5) 55 6.4 (4.0, 10.2)
   Single ventricle 141 3 9.6 (1.8, 32.2) 12 29.6 (13.5, 61.7)

Note: Bold font represents a statistically significant finding; italicized font represents a crude odds ratio.

Abbreviations: ASD, atrial septal defect; CI, confidence interval; DORV-TGA, double outlet right ventricle with transposition of the great arteries; d-TGA, d-transposition of the great arteries; HLHS, hypoplastic left heart syndrome; LVOTO, left ventricular outflow tract obstruction; NC, not calculated; OR, odds ratio; RVOTO, right ventricular outflow tract obstruction; TAPVR, total anomalous pulmonary venous return; VSD, ventricular septal defect.

a

The pregestational type 1 analysis included 24 exposed and 10,840 unexposed controls. The pregestational type 2 analyses included 34 exposed and 10,840 unexposed controls.

b

Crude ORs and Fisher's Exact 95% CIs are presented for defects groups with 3–4 exposed cases and are italicized. For defects with ≥5 exposed cases, Firth's penalized likelihood estimates were adjusted for mother's age, race/ethnicity, education, body mass index (weight in kg/height in m), and study center. Estimates are not provided for analyses with <3 exposed cases.

c

The number of controls differed for the following type 1 birth defect analyses: pulmonary valve stenosis (21 exposed, 10,401 unexposed controls) and perimembranous VSD (14 exposed and 9,792 unexposed controls).

d

The number of controls differed for the following type 2 birth defect analyses: conoventricular VSD (16 exposed and 6,340 unexposed controls), pulmonary valve stenosis (34 exposed and 10,401 unexposed controls), perimembranous VSD (16 exposed and 6,340 unexposed controls).