Table 2.

Evaluation of disease activity score or clinical symptoms in 16 patients

No	Diagnosis	3 months before	Baseline	3 months	6 months	9 months	12 months
1	AGSa	3	3	3	3	3	3
2	AGSa	1.26	3	3	3	3	3
3	AGSa	0.2	0.2	0	0	-	-
4	Blau syndromeb	0	0	0	0	0	0
5	Blau syndromeb	6	12	12	-	-	-
6	Blau syndromeb	0	0	0	0	0	0
7	Blau syndromeb	30	30	12	4	-	-
8	CINCAc	35	28	10	8	2	4
9	CINCAc	7	7	14	5	0	0
10	DADA2	Persistent fever, rash, oral ulcers and celialgia	Persistent fever, rash, oral ulcers and celialgia	Reduced fever frequency	Fever and celialgia improved	Few ulcers and rashes remained	Disappearance of rash
11	FMFc	15	15	0	0	0	0
12	HA20d	Mild	Mild	Disease-free activity	Disease-free activity	Disease-free activity	Disease-free activity
13	HA20d	Moderate	Moderate	Mild	Disease-free activity	Moderate	Disease-free activity
14	PLAID	Recurrent fevers and rash	Recurrent fevers and rash	Intermittent fever, rash and arthralgia	Intermittent fever, rash and arthralgia	Occasional fever and rash	Occasional fever and rash
15	SAVIe	3	3	1	2	2	-
16	TRAPSc	15	15	15	10	15	10

^aClinical score of AGS

^bNumber of active arthritis episodes

^cAIDAI

^dDisease severity of HA20

^eDisease activity rating scale of SAVI