TABLE 2.

Phenotypic, audiological, and implantation characteristics of probands and implanted ears

		n	%
Subjects		76
Phenotypic characteristics
Sex	Male	35	46.1
	Female	41	53.9
Age	0–9 y	16	21.1
	10–29 y	21	27.6
	30–59 y	26	34.2
	60–80+ y	13	17.1
Onset of hearing loss	Congenital	35	46.0
	Pre/perilingual (0–6)	13	17.1
	Postlingual (>6–19)	16	21.1
	Postlingual (≥20–59)	12	15.8
Laterality of hearing loss	Bilateral symmetric	70	92.1
	Bilateral asymmetric	2	2.6
	Single-sided deafness	4	5.3
Ethnicity	Western European	52	68.4
	Western Asian	10	13.2
	Eastern European	8	10.5
	Southern European	5	6.6
	Southern Asian	1	1.3
Family history	Autosomal-recessive	25	32.9
	Autosomal-dominant	14	18.4
	X-linked	2	2.6
	Sporadic	35	46.1
Ears implanted		123
Characteristics of implanted ears
Side of cochlear implant	Left	59	48.0
	Right	64	52.0
Preoperative grades of hearing loss for implanted ears	Moderately severe	1	0.8
	Severe	5	4.1
	Profound	24	19.5
	Complete	93	75.6
Age at implantation	0–2 y	31	25.2
	3–5 y	14	11.4
	6–59 y	66	53.7
	≥60 y	12	9.7
Time delay between age of hearing loss onset vs. age at implantation	≤1 y	21	17.0
	2–5 y	26	21.2
	6–29 y	45	36.6
	30–69 y	31	25.2
Laterality of cochlear implantation	Unilateral	29	23.6
	Bilateral simultaneous	15	12.2
	Bilateral sequential	32	26.0
	Bilateral all	47	38.2