Table 2.

The Age-stratified and Sex-stratified Incidences and Incidence Rate of Pseudoxanthoma Elasticum in Japan from 2011 to 2020, as Determined by the National Database of the Health Insurance Claims and Specific Health Checkups of Japan

Age Groups (Years)	Japanese Population∗			Incidence			Incidence Rate (95% CI)†
	Male	Female	Total	Male	Female	Total	Male	Female	Total
0–29	17 149	16 230	33 378	18	50	68	0.01 (0–0.03)	0.03 (0–0.06)	0.02 (0.01–0.04)
30–39	7127	6880	14 007	12	45	57	0.02 (−0.01 to 0.05)	0.07 (0–0.13)	0.04 (0.01–0.07)
40–44	4261	4157	8419	13	33	46	0.03 (−0.02 to 0.08)	0.08 (−0.01 to 0.17)	0.05 (0–0.1)
45–49	4951	4846	9797	17	41	58	0.03 (−0.02 to 0.09)	0.08 (0–0.17)	0.06 (0.01–0.11)
50–54	4366	4318	8684	26	42	68	0.06 (−0.01 to 0.13)	0.10 (0–0.19)	0.08 (0.02–0.14)
55–59	3932	3940	7872	20	54	74	0.05 (−0.02 to 0.12)	0.14 (0.02–0.25)	0.09 (0.03–0.16)
60–64	3667	3764	7431	41	63	104	0.11 (0–0.22)	0.17 (0.04–0.30)	0.14 (0.05–0.23)
65–69	4015	4268	8283	31	83	114	0.08 (−0.01 to 0.16)	0.19 (0.06–0.33)	0.14 (0.06–0.22)
70–74	4332	4846	9178	29	146	175	0.07 (−0.01 to 0.14)	0.30 (0.15–0.46)	0.19 (0.10–0.28)
75–79	3182	3939	7120	15	88	103	0.05 (−0.03 to 0.12)	0.22 (0.08–0.37)	0.14 (0.06–0.23)
80–84	2248	3168	5416	16	66	82	0.07 (−0.04 to 0.18)	0.21 (0.05–0.37)	0.15 (0.05–0.26)
> 85	1951	4216	6168	10	61	71	0.05 (−0.05 to 0.15)	0.14 (0.33–0.26)	0.12 (0.03–0.20)
All patients	61 181	64 572	125 753	248	772	1020	0.04 (0.02–0.06)	0.12 (0.09–0.15)	0.08 (0.07–0.10)

^∗Japanese population data (as of October 1, 2020) were based on the Japanese Ministry of Internal Affairs and Communications. (Unit: 1000 people).

^†The incidence rate is reported per 100 000 person-years. CI = confidence interval.