Table 4.

The Age-stratified and Sex-stratified Number of Living Patients and Prevalence of Pseudoxanthoma Elasticum in Japan from 2011 to 2020, as Determined by the National Database of the Health Insurance Claims and Specific Health Checkups of Japan

Age Groups (Years)	Japanese Population∗			Number of Living Patients			Prevalence (95% CI)†
	Male	Female	Total	Male	Female	Total	Male	Female	Total
0–29	17 149	16 230	33 378	18	51	69	0.10 (0.06–0.15)	0.31 (0.23–0.40)	0.21 (0.16–0.26)
30–39	7127	6880	14 007	12	47	59	0.17 (0.07–0.26)	0.68 (0.49–0.88)	0.42 (0.31–0.53)
40–44	4261	4157	8419	14	33	47	0.33 (0.16–0.50)	0.79 (0.52–1.06)	0.56 (0.40–0.72)
45–49	4951	4846	9797	17	43	60	0.34 (0.18–0.51)	0.89 (0.62–1.15)	0.61 (0.46–0.77)
50–54	4366	4318	8684	23	49	72	0.53 (0.31–0.74)	1.13 (0.82–1.45)	0.83 (0.64–1.02)
55–59	3932	3940	7872	19	57	76	0.48 (0.27–0.70)	1.45 (1.07–1.82)	0.97 (0.75–1.18)
60–64	3667	3764	7431	40	65	105	1.09 (0.75–1.43)	1.73 (1.31–2.15)	1.41 (1.14–1.68)
65–69	4015	4268	8283	35	90	125	0.87 (0.58–1.16)	2.11 (1.67–2.54)	1.51 (1.24–1.77)
70–74	4332	4846	9178	27	154	181	0.62 (0.39–0.86)	3.18 (2.68–3.68)	1.97 (1.68–2.26)
75–79	3182	3939	7120	15	83	98	0.47 (0.23–0.71)	2.11 (1.65–2.56)	1.38 (1.10–1.65)
80–84	2248	3168	5416	18	64	82	0.80 (0.43–1.17)	2.02 (1.53–2.52)	1.51 (1.19–1.84)
> 85	1951	4216	6168	10	66	76	0.51 (0.19–0.83)	1.57 (1.19–1.94)	1.23 (0.96–1.51)
All patients	61 181	64 572	125 753	248	802	1050	0.41 (0.35–0.46)	1.24 (1.16–1.33)	0.83 (0.78–0.89)

^∗Japanese population data (as of October 1, 2020) were based on the Japanese Ministry of Internal Affairs and Communications. (Unit: 1000 people).

^†The prevalence is reported per 100 000 persons. CI = confidence interval.