Table 1.

Names for vasculitides adopted by the 2012 International Chapel Hill Consensus Conference on the Nomenclature of Vasculitides [2]

Large vessel vasculitis

Takayasu arteritis

Giant cell arteritis

Medium vessel vasculitis

Polyarteritis nodosa

Kawasaki disease

Small vessel vasculitis

ANCA-associated vasculitis • Microscopic polyangiitis • Granulomatosis with polyangiitis (Wegener’s) • Eosinophilic granulomatosis with polyangiitis (Churg Strauss)

Immune complex small vessel vasculitis • Antiglomerular basement membrane disease • Cryoglobulinemic vasculitis • IgA vasculitis (Henoch-Schönlein) • Hypocomplementemic urticarial vasculitis

Variable vessel vasculitis

Behcet’s disease

Cogan’s syndrome

Single-organ vasculitis

Cutaneous leukocytoclastic angiitis

Cutaneous arteritis

Primary central nervous system vasculitis

Isolated aortitis

Others

Vasculitis associated with systemic disease

Lupus vasculitis

Rheumatoid vasculitis

Sarcoid vasculitis

Others

Vasculitis associated with probable etiology

Hepatitis C virus-associated cryoglobulinemic vasculitis

Hepatitis B virus-associated vasculitis

Syphilis-associated aortitis

Drug-associated immune complex vasculitis

Drug-associated ANCA-associated vasculitis

Cancer-associated vasculitis

Others