Figure 7.

Representative case with a thin retina but good visual acuity and full-field stimulus testing (FST) sensitivity. The average retinal thickness (RET) (B) was 184 μm, and OCT images (A) revealed severe photoreceptor cell loss at the fovea. Visual acuity was counting fingers (CF), the highest category of this study, and the FST sensitivities (C) were similar to those of normal eyes, with a high sensitivity to blue light. The response to chromatic pupillometry (D) was also good with rod response, which was rare in our study cohort and the Goldman visual field test (E) showed a relatively large residual field of view in the periphery. RET = retina; ONL = outer nuclear layer; INL = inner nuclear layer; GCL = ganglion cell layer