Table 5.
Posterior segment findings of cases of Axenfeld-Rieger syndrome (N = 10)
| Sl. No. |
Fundus findings
|
OCT-RNFL
|
B-Scanb
|
||
|
RE
|
LE
|
RE
|
LE
|
||
| Case 1 | C:D 0.9 | Glaucomatous Optic Atrophy | CNBA | CNBA | ND |
| Case 2 | a | No view due to hazy media | a | CNBA | ND |
| Case 3 | C:D 0.8 | No view due to hazy media | CNBA | CNBA | ND |
| Case 4 | C:D 0.4 | No view due to hazy media | CNBA | CNBA | WNL BE |
| Case 5 | C:D 0.3 | C:D 0.3 | WNL | WNL | WNL BE |
| Case 6 | C:D 0.6 | C:D 0.6 | WNL | WNL | WNL BE |
| Case 7 | C:D 0.9 | C:D 0.9 | CNBA | CNBA | WNL BE |
| Case 8 | C:D 0.8, Tilted Disc, Peripapillary Atrophy | C:D 0.8, Tilted Disc, Peripapillary Atrophy | CNBA | CNBA | WNL BE |
| Case 9 | C:D 0.8, Circumferential NRR thinning | C:D 0.8, Circumferential NRR thinning | CNBA | CNBA | WNL BE |
| Case 10 | C:D 0.5 | C:D 0.5 | WNL | WNL | WNL BE |
Eye lost to trauma.
Comments on vitreous, retinochoroid and sclera on B-scan USG.
Optic nerve head findings are as clinically correlated. C:D: Cup: Disc ratio; NRR: Neuroretinal rim; CNBA: Could not be acquired; ND: Not done; WNL: Within normal limits.