TABLE 3.
Cumulative mortality | Wilson's disease patients | Reference individuals | ||||
---|---|---|---|---|---|---|
1 year | 5 years | 10 years | 1 year | 5 years | 10 years | |
All | 0.0 (−) | 5.6 (2.7–11.5) | 9.3 (5.0–16.8) | 0.4 (0.2–0.9) | 1.5 (1.0–2.3) | 2.4 (1.6–3.6) |
Men | 0.0 (−) | 6.2 (2.4–15.6) | 8.6 (3.6–19.9) | 0.3 (0.1–1.1) | 1.5 (0.8–2.8) | 1.8 (1.0–3.4) |
Women | 0.0 (−) | 5.1 (1.7–15.0) | 10.0 (4.2–22.7) | 0.6 (0.2–1.5) | 1.4 (0.7–2.7) | 3.1 (1.8–5.2) |
Age <20 years | 0.0 (−) | 0.0 (−) | 0.0 (−) | 0.0 (−) | 0.2 (0.0–1.6) | 0.2 (0.0–1.6) |
Age ≥20 years | 0.0 (−) | 8.1 (3.9–16.2) | 12.7 (7.0–22.5) | 0.6 (0.3–1.4) | 2.1 (1.3–3.3) | 3.3 (2.2–5.0) |
Wilson's disease, born in Sweden | 0 (−) | 5.6 (2.4–12.9) | 10.8 (5.4–20.9) | 0.3 (0.1–1.0) | 1.5 (0.9–2.5) | 2.5 (1.5–4.0) |
Wilson's disease, born outside Sweden | 0 (−) | 5.8 (1.5–21.5) | 5.8 (1.5–21.5) | 0.7 (0.2–2.0) | 1.5 (0.7–3.2) | 2.3 (1.1–4.8) |
Neuropsychiatric condition | 0 (−) | 12.5 (5.4–27.5) | 20.7 (10.0–39.7) | 0.6 (0.2–1.9) | 1.7 (0.8–3.6) | 3.5 (1.9–6.4) |
No neuropsychiatric condition | 0 (−) | 2.4 (0.6–9.3) | 4.1 (1.3–12.3) | 0.3 (0.1–1.0) | 1.4 (0.8–2.4) | 2.0 (1.2–3.4) |
Note: Results are in per cent.