Table 1.
Patients’ characteristics
| Characteristics | Patients with total anomalous pulmonary venous connection (n = 57) |
|---|---|
| Female | 28 (49) |
| Type of TAPVC | |
| Supracardiac | 26 (46) |
| Cardiac | 6 (11) |
| Infracardiac | 11 (19) |
| Unknown | 14 (25) |
| Associated lesions | |
| None/unknown | 17 (29) |
| Ductus arteriosus | 5 (9) |
| VSD | 2 (4) |
| PLSVC | 1 (2) |
| ASD | 32 (56) |
| Pulmonary venous obstruction preoperatively | 14 (25) |
| Preoperative complications | |
| Pulmonary hypertension | 10 (18) |
| Valvulopathy∗ | 6 (11) |
| Arrhythmia | 0 |
| Median age at correction (mo) | 1 (1 d-14 y) |
| Median time since surgery (y) | 21 (8-51) |
| Median age at latest follow-up (y) | 20 (16-67) |
| Symptomatic at latest follow-up | 12 (21) |
| NYHA class II | 4 (7) |
| Palpitations | 6 (11) |
| Chest pain | 5 (9) |
| Treatment at latest follow-up | 4 (7) |
| Beta-blocker | 3 (5) |
| Calcium channel blocker | 1 (2) |
| Anticoagulation | 1 (2) |
Data are expressed in n (%) and median (interquartile range).
ASD, atrial septal defect; PLSVC, persistent left superior vena cava; TAPVC, total anomalous pulmonary venous connection; VSD, ventricular septal defect.
∗
Tricuspid regurgitation in 3 (1 severe and 2 unknown), severe mitral regurgitation in 1, pulmonary stenosis in 1, and unknown in 1.