Skip to main content
. 2023 Jul 1;75(4):4007–4011. doi: 10.1007/s12070-023-03997-7

Table 3.

Comparison of cases of ANCA-associated vasculitis overlapping with large vessel vasculitis

Characteristics Patient 1 [7] Patient 2 [7] Patient 3 [7] Patient 4 [7] Patient 5 [7] Our patient
Age (years) 66 52 76 63 46 32
Sex Female Female Female Male Female Male
ANCA associated vasculitis GPA GPA GPA GPA GPA GPA
Large vessel vasculitis Aortitis Temporal arteritis Temporal arteritis Temporal arteritis Aotitis Aortitis Arch and abdominal
Clinical manifestation
ENT Sinusitis Sinusitis NCD, SGS Crusts, OPT Nasal Polyp Otitis media, hearing loss
Renal – Hematuria Hematuria – – Hematuria
Pulmonary Nodules/ infiltrate – Nodules Nodules – Infiltrate
Neurologic – Pachymeningitis – – – VII cranial nerve palsy
Joints Arthritis – – – – –
Laboratory
ANCA cANCA-PR3 cANCA-PR3 pANCA-MPO cANCA-PR3 cANCA-PR3 cANCA-PR3
ESR mm/hr 85 67 84
CRP mg/l 176 120 28.7
Treatment Corticosteroid + Cyclophosphamide Corticosteroid + Rituximab Corticosteroid + Methotrexate Corticosteroid + Methotrexate Corticosteroid + Cyclophosphamide Corticosteroid + Cyclophosphamide

GPA: Granulomatosis with polyangiitis, NCD: nasal cartilage destruction, SGS: subglottic stenosis, OPT: orbit pseudotumor