Table 3.
Comparison of cases of ANCA-associated vasculitis overlapping with large vessel vasculitis
| Characteristics | Patient 1 [7] | Patient 2 [7] | Patient 3 [7] | Patient 4 [7] | Patient 5 [7] | Our patient |
|---|---|---|---|---|---|---|
| Age (years) | 66 | 52 | 76 | 63 | 46 | 32 |
| Sex | Female | Female | Female | Male | Female | Male |
| ANCA associated vasculitis | GPA | GPA | GPA | GPA | GPA | GPA |
| Large vessel vasculitis | Aortitis | Temporal arteritis | Temporal arteritis | Temporal arteritis | Aotitis | Aortitis Arch and abdominal |
| Clinical manifestation | ||||||
| ENT | Sinusitis | Sinusitis | NCD, SGS | Crusts, OPT | Nasal Polyp | Otitis media, hearing loss |
| Renal | – | Hematuria | Hematuria | – | – | Hematuria |
| Pulmonary | Nodules/ infiltrate | – | Nodules | Nodules | – | Infiltrate |
| Neurologic | – | Pachymeningitis | – | – | – | VII cranial nerve palsy |
| Joints | Arthritis | – | – | – | – | – |
| Laboratory | ||||||
| ANCA | cANCA-PR3 | cANCA-PR3 | pANCA-MPO | cANCA-PR3 | cANCA-PR3 | cANCA-PR3 |
| ESR mm/hr | 85 | 67 | 84 | |||
| CRP mg/l | 176 | 120 | 28.7 | |||
| Treatment | Corticosteroid + Cyclophosphamide | Corticosteroid + Rituximab | Corticosteroid + Methotrexate | Corticosteroid + Methotrexate | Corticosteroid + Cyclophosphamide | Corticosteroid + Cyclophosphamide |
GPA: Granulomatosis with polyangiitis, NCD: nasal cartilage destruction, SGS: subglottic stenosis, OPT: orbit pseudotumor