Table 1.

Differential diagnosis of urticaria.

Conditions presenting with urticaria
•Anaphylaxis •Exercise-induced anaphylaxis •Acute urticaria • Chronic urticaria - Chronic spontaneous urticaria - Chronic inducible urticaria •Contact Urticaria/Urticarial Contact Dermatitis •Mast cell activation syndrome
Conditions presenting with urticarial lesions
•Serum sickness-like reaction •Kawasaki disease •Papular urticaria •Urticaria Multiforme •Juvenile idiopathic arthritis •Mastocytosis •Urticarial vasculitis • Autoinflammatory urticarial syndromes - Cryopyrin associated periodic syndrome (CAPS) - TNF receptor-associated periodic syndrome (TRAPS) - Mevalonate kinase deficiency (Hyper IgD syndrome) - Periodic fever, aphthous stomatitis, pharyngitis, and adenitis syndrome (PFAPA) - Schnitzler syndrome - Adult Onset Still’s Disease (AOSD) •Wells syndrome and hyper-eosinophilic syndrome •Bullous pemphigoid •Frey syndrome