Figure 1.
Patient 1 had a large kaposiform hemangioendothelioma on her left upper arm (A), and the mass showed improvement after nine months of sirolimus administration (B). In this T2-weighted MRI, patient 3, who presented with a large cystic mass on the lower left neck and around the airway (indicated by the arrow) at birth (C), experienced relief from airway compression after 5 months of sirolimus treatment (D). Patient 4 showed a protruding mass suspected to be a lymphatic malformation on the right forehead and eyelid (E), and a T2-weighted MRI was obtained after 6 months of sirolimus treatment (F).