Fig. 1.

Patient 1 of LCHADD complicated with CNV in the right eye. A, Color fundus photograph revealing a nummular hyperpigmented lesion in the right macula with a scar temporal and superonasal to the pigmented lesion. B, Color fundus photograph of the same patient after 22 years follow up showing extension of the dense hyperpigmented lesion and faint scar surrounded by a pale macular choroidal atrophy. C, After applying the projection resolved algorithm to a 6 × 6 mm red box area in B, color-coded composite en face OCTA, subretinal choroidal neovascular plexus (yellow) was highlighted D, Cross-sectional Spectral Domain-OCTA image corresponding to the white dot line in C showing subfoveal choroidal neovascularization. E, En-face slab of choriocapillaris showing an enlarged area of subfoveal CNV network. F, En-face OCT slab of the photoreceptor demonstrated subretinal fibrotic scar. Retinal tubulation adjacent to the CNV were observed. (yellow arrow). (For interpretation of the references to color in this figure legend, the reader is referred to the Web version of this article.)