TABLE 3.

Results of EMG/NCS in cases with APBD.

Case	Age (years)	Summary of EMG/NCS findings
Case 1	54.4	Length-dependent motor greater than sensory axonal neuropathy with chronic neurogenic changes in the right lower extremity
	54.7	Length-dependent, axonal, sensorimotor peripheral neuropathy
Case 2	62.2	Moderately severe, predominantly axonal, sensorimotor polyneuropathy without evidence of lumbosacral radiculopathy
	64.7	Severe axonal neuropathy in the legs with chronic neurogenic changes in the needle EMG to the proximal and distal leg muscles. Carpal tunnel in the right hand as well as mild ulnar sensory neuropathy
Case 3	*	Generalized axonal sensorimotor polyneuropathy with L4–5 radiculopathy
	61.2	Motor-predominant axonal polyneuropathy vs. radiculopathy. Abnormal conduction in descending corticospinal tracts
Case 4	31.0	Length-dependent motor and sensory axonal neuropathy with chronic neurogenic changes involving the lower limbs
Case 5	50.0	Length-dependent, moderate axonal sensorimotor peripheral neuropathy involving the lower and upper limbs
Case 6	47.0	Length-dependent, mild axonal sensorimotor peripheral neuropathy with motor predominance involving the lower and upper limbs
Case 7	71.0	Length-dependent, mild axonal sensorimotor peripheral neuropathy with sensory predominance involving the lower and upper limbs

*Represents result at an undisclosed age prior to initial clinical evaluation available for review.