Table 2.
Potential liver complications in autosomal dominant polycystic kidney disease
Acute Complications from Single Cysts | Severe Hepatomegaly | Other Liver Complications |
---|---|---|
Infection or torsion Rupture or hemorrhage Obstructive jaundice Ascending cholangitis Biliary peritonitis (after cyst rupture) |
Abdominal fullness Abdominal distension GERD/anorexia/nausea/early satiety Dyspnea Abdominal hernia LFT abnormalities Ascites, hepatic outflow obstruction, portal hypertension, IVC compression, bile duct compression Pleural effusion Organ displacement Failure to thrive/malnutrition Budd-Chiari syndrome |
Isolated common bile duct dilation Hepatic fibrosis or biliary fibroadenomatosis Idiopathic biliary tract dilation (Caroli syndrome) |
GERD, gastroesophageal reflux disease, LFT; liver function test; IVC, inferior vena cava.