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. 2023 Nov 27;4(12):1806–1815. doi: 10.34067/KID.0000000000000296

Table 2.

Potential liver complications in autosomal dominant polycystic kidney disease

Acute Complications from Single Cysts Severe Hepatomegaly Other Liver Complications
Infection or torsion
Rupture or hemorrhage
Obstructive jaundice
Ascending cholangitis
Biliary peritonitis (after cyst rupture)
Abdominal fullness
Abdominal distension
GERD/anorexia/nausea/early satiety
Dyspnea Abdominal hernia
LFT abnormalities
Ascites, hepatic outflow obstruction,
portal hypertension, IVC compression,
bile duct compression
Pleural effusion
Organ displacement
Failure to thrive/malnutrition
Budd-Chiari syndrome
Isolated common bile duct dilation
Hepatic fibrosis or biliary fibroadenomatosis
Idiopathic biliary tract dilation (Caroli syndrome)

GERD, gastroesophageal reflux disease, LFT; liver function test; IVC, inferior vena cava.