Table 2.
Baseline characteristics
| Clinical characteristics | Total cohort N=285 | No of observations |
| Age at baseline visit—years | 34±14 | 285 |
| Age at repair—years | 6 (1–6) | 285 |
| Type of repair | ||
| Non transannular patch | 118 (40%) | |
| Transannular patch | 110 (37%) | |
| RV-PA conduit | 56 (19%) | |
| Unknown | 10 (3%) | |
| Female | 126 (44%) | |
| BMI—kg/m2 | 24.2±4.8 | |
| NYHA functional class | ||
| I | 229 (80%) | |
| II or III | 56 (20%) | |
| NT-proBNP—pg/mL | 133 (66–262) | 217 |
| Sinus rhythm | 259 (91%) | |
| Atrial fibrillation or flutter | 10 (4%) | |
| Pacemaker rhythm | 12 (4%) | |
| QRS duration—ms | 143±26 | 281 |
| Echocardiography data | ||
| LVEDD—mm | 47±7 | 275 |
| LVESD—mm | 32±7 | 273 |
| LAVI—mL/m2 | 24±15 | 280 |
| RAA—cm2 | 19±7 | 247 |
| LVEF—% | 59±8 | 280 |
| RV FAC—% | 39±8 | 272 |
| RV-RA gradient—mm Hg | 31±12 | 254 |
| Tricuspid regurgitation>mild | 260 (91%) | 275 |
| Pulmonary regurgitation<severe | 226 (79%) | 273 |
| Strain and dyssynchrony | ||
| RV GLS—% | −15.4±5 | 222 |
| RV Dyssynchrony Index—ms | 40 (28–52) | 222 |
| Max RV Delay—ms | 95 (62–127) | 222 |
| IVED—ms | −3±19 | 260 |
| IVSD—ms | 105±52 | 209 |
| CMR data | ||
| LV EDVI—mL | 88±21 | 185 |
| RV EDVI—mL | 126±35 | 201 |
| RVEF—% | 48±9 | 208 |
| LVEF—% | 57±8 | 206 |
| Exercise data | ||
| Peak heart rate—bpm | 158±27 | 235 |
| Peak VO2—mL/kg/min | 22±9 | 237 |
| VE/VCO2 slope | 27±5 | 232 |
Data are expressed as N (% of total), mean±SD or median (IQR) unless otherwise specified. The number of observations refers to the available data in the registry.
BMI, body mass index; CMR, cardiac MR; EDV, end-diastolic volume; EDVI, end-diastolic volume indexed; GLS, global longitudinal strain; IVED, interventricular ejection delay; IVSD, interventricular shortening delay; LAVI, left atrial volume indexed; LVEDD, left ventricular end-diastolic diameter; LVEF, left ventricular ejection fraction; LVESD, left ventricular end-systolic diameter; NT-proBNP, N-terminal pro–B-type natriuretic peptide; NYHA, New York Heart Association; RAA, right atrial area; RVEF, right ventricular ejection fraction; RV FAC, RV fractional area change; VE/VCO2, minute ventilation/carbon dioxide output; VO2, oxygen uptake.