Table 2.
SQTS diagnostic criteria (a score of ≥ 3 indicates a moderate-to-high probability of SQTS).
| SQTS Diagnostic Criteria | Points |
|---|---|
| QTc interval (ms) | |
| <370 | 1 |
| <350 | 2 |
| <330 | 3 |
| J-point-to-T peak interval < 120 ms | 1 |
| Family history * | |
| SQTS high-probability in a first- or second-degree relative | 2 |
| Autopsy-negative SCD in a first- or second-degree relative | 1 |
| SIDS | 1 |
| Genotype | |
| Genotype positive | 2 |
| Mutation of undetermined significance in a culprit gene | 1 |
* ECG should be recorded in the absence of medications or disorders known to prolong QTc. SIDS: sudden infant death syndrome; SQTS: short QT syndrome.