Table 10.
Treatment of genetic vitamin-D dependent rickets.
Vitamin D or Metabolites | Calcium Salt | |
---|---|---|
Vitamin D dependent rickets type 1A | Alfacalcidiol or calcitriol 10–100 ng/kg/day | 0.5–3 g/day in 2–3 doses |
Vitamin D dependent rickets type 1 B | Homozygous patient: vitamin D 600,000 IU/every 3 months | 0.5–2 g/day in 2–3 doses |
Heterozygous patients: vitamin D 5000–10,000 IU/day or | ||
Calcifediol 15–50 µg/day | ||
Vitamin D dependet rickets type 2 | Calcitriol or alfacalcidol 10–400 ng/kg/day | 3–6 g/day in 2–3 doses |
Vitamin D dependent rickets type 3 | Vitamin D 20,000–50,000/day |