Table 1.
Patient characteristics
| Characteristic | N = 19 |
|---|---|
| Age (at enrollment) | |
| Mean (SD) | 55 (15) |
| Median (Range) | 57 (24, 75) |
| Sex | |
| F | 11 (58%) |
| M | 8 (42%) |
| Race | |
| Black | 1 (5.3%) |
| White | 18 (95%) |
| FVC (prior to start) | |
| Mean (SD) | 3.04 (0.83) |
| Median (Range) | 3.09 (1.57, 4.75) |
| Unknown | 2 |
| FEV1 (prior to start) | |
| Mean (SD) | 2.38 (0.53) |
| Median (Range) | 2.36 (1.45, 3.48) |
| Unknown | 1 |
| ILD Type | |
| Chronic Hypersensitivity Pneumonitis | 1 (5.3%) |
| CPFE | 2 (11%) |
| CTD-ILD | 3 (16%) |
| Idiopathic NSIP | 1 (5.3%) |
| ILD | 1 (5.3%) |
| IPF | 4 (21%) |
| LAM | 2 (11%) |
| NSIP | 1 (5.3%) |
| Sarcoidosis | 2 (11%) |
| Unclassifiable | 2 (11%) |
n (%)
CPFE Combined Pulmonary Fibrosis and Emphysema
CTD−ILD Connective Tissue Disease−related Interstitial Lung Disease
FEV1 Forced Expiratory Volume in 1 s
FVC Forced Vital Capacity
ILD Interstitial Lung Disease
IPF Idiopathic Pulmonary Fibrosis
LAM Lymphangioleiomyomatosis
NSIP Non−Specific Interstitial Pneumonia