Table 1.
Characteristic | Values (N = 108) |
---|---|
Age at the time of procedure (y), median (IQR) | 15.8 (8.3-17.6) |
Sex, n (%) | |
Female | 81 (75.6) |
Race, n (%) | |
Asian | 1 (0.9) |
Black or African American | 15 (14.0) |
White or Caucasian | 83 (77.6) |
Multiracial | 1 (0.9) |
Not known, unlisted | 7 (6.5) |
Ethnicity, n (%) | |
Hispanic/Latino | 20 (18.7) |
Age at diagnosis, median (IQR) | 14.0 (7.7-16.3) |
Blood type, n (%) | |
A | 18 (16.8) |
B | 4 (3.7) |
AB | 0 (0) |
O | 54 (50.5) |
Unknown | 31 (29.0) |
Diagnostic laboratory values,a median (IQR) | |
FVIII (n = 108) | 90 (78-108.5) |
VWF:Ag (n = 108) | 56 (48-62) |
VWF:RCo (n = 108) | 41 (37.5-45) |
VWF:GPIbM (n = 80) | 48 (43-54) |
VWF:CB (n = 8) | 46 (41.75-52) |
Isolated low VWF:RCo, n (%) | 33 (30.8) |
Isolated low VWF:RCo, other functional level drawn, and normal, n (%) | 26 (24.3) |
Number of times VWD levels drawn in the timeframe, median (IQR) | 2 (2-3) |
Bleeding score, median (IQR) | 4 (3-5) |
Ag, antigen; CB, collagen binding; FVIII, factor VIII; GP, glycoprotein; RCo, ristocetin cofactor; VWD, von Willebrand disease; VWF, von Willebrand factor.
Earliest full set of diagnostic levels.