Table 1.

This table summarizes the main medical and surgical treatments for extrarenal involvement in ADPKD patients. IPMN: intraductal papillary mucinous neoplasm. ACs: arachnoid cysts. ACEi: angiotensin converting enzyme inhibitors. ARB: angiotensin receptor blockers. MRA: mineralocorticoid receptor antagonist.

Organ	Medical Therapy	Surgical Treatment
Liver	Somatostatin analogues	Aspiration sclerotherapy Fenestration Hepatic resection Liver transplant
Pancreas	Insulin Replacement pancreatic enzymes	Resection of malignant IPMN
Spleen	---	---
Brain	---	AC removal
Vascular	---	Evaluated on a case-by-case basis
Heart	ACEi, ARB, or MRA	Surgical correction
Bone	---	---