Fundus features of Coats-like vasculopathy (CLV) in inherited retinal disease (IRD). A, Patient ID 59 at 7 years of age. A retinal dystrophy affecting both the macula and peripheral retina is evident, with bilateral exudation in the nasal and inferior retina. This patient had negative genetic testing results and a syndromic IRD with developmental delay, maxillary and mandibular hypoplasia, and pontocerebellar atrophy. B, Patient ID 2 with GNAT2-related achromatopsia at 35 years of age. Peripheral atrophy with exudation is visible unilaterally in the right eye (OD). C, The OD of patient ID 13 at 13 and 18 years of age. We see the development of retinal exudation and telangiectasia over time in the superotemporal quadrant. She had negative genetic testing and a more severely affected left eye, with recurrent vitreous hemorrhages. D, Fluorescein angiogram and color retinal imaging of the OD of patient ID 7 at 15 years old. Temporal nonperfusion and telangiectasia are visible. Color imaging is positive for retinal exudation and atrophy in 3 retinal quadrants. Genetic testing was not performed.