Table 3. Criteria for diagnosis of FMF .

Adapted with permission from Livneh et al. [6]

FMF: familial Mediterranean fever.

A	Major criteria
	Typical attacks
1	Peritonitis (generalized)
2	Pleuritis (unilateral) or pericarditis
3	Monoarthritis (hip, knee, ankle)
4	Fever alone
	Typical attack recurrent ≥ 3, fever of 38 °C or > rectal, and short (between 12 hours and 3 days)
B	Minor criteria
	Incomplete attacks
1	Abdomen
2	Chest
3	Joint
4	Exertional leg pain
5	Favorable response to colchicine
C	Supportive criteria
1	Family history of FMF
2	Appropriate ethnic origin
3	Age less than 20 years at the time of diagnosis
4	Severe requiring bed rest
5	Spontaneous remission
6	Symptoms free intervals
7	Transient inflammatory response (WBCs, ESR, fibrinogen, or serum amyloid A)
8	Episodic hematuria or proteinuria
9	Negative laparotomy or appendectomy
10	Consanguinity of the parents
D	≥1 Major criteria, ≥2 minor criteria, 1 minor plus 5 supportive criteria