Table 1.

Pulmonary hypertension groups. PAH: pulmonary arterial hypertension; PH: pulmonary hypertension; CCB: calcium channel blocker; LHD: left heart disease; PA: pulmonary artery

GROUP	SUBTYPES	GENERAL PREVALENCE	TREATMENT STRATEGIES
1 PAH	Idiopathic Heritable Associated with drugs/toxins Associated with connective tissues disease Venous/capillary involvement Persistent PH of newborn	Rare	PAH medications CCB (select patients) Lung transplantation
2 PH associated with LHD	Heart failure Valvular disease Congenital/acquired cardiovascular conditions	Very common	Treatment of LHD Consider PAH medications
3 PH associated with lung disease and/or hypoxia	Obstructive Restrictive Mixed obstructive/restrictive Hypoventilation syndromes Hypoxia without lung disease Developmental lung disorders	Common	Treat underlying lung disease Consider PAH medications
4 PH associated with pulmonary artery obstructions	Chronic thromboembolic Other PA obstructions	Rare	Pulmonary endarterectomy Balloon pulmonary angioplasty Consideration medications
5 PH with unclear/multifactorial etiology	Hematological Systemic Metabolic Chronic renal failure with or without dialysis Pulmonary tumor thrombotic microangiopathy Fibrosing mediastinitis	Rare	Treatment of underlying disease Consider PAH medications