Table 4.
Survival
| 1 year, % (95% CI) | 5 years, % (95% CI) | 10 years, % (95% CI) | 15 years, % (95% CI) | |
|---|---|---|---|---|
| NS | 94.3 (87.7–97.4) | 91.3 (83.9–95.4) | 91.3 (83.9–95.4) | 91.3 (83.9–95.4) |
| NSML | 91.7 (53.9–98.8) | 91.7 (53.9–98.8) | 91.7 (53.9–98.8) | 91.7 (53.9–98.8) |
| CS | 81.8 (23.9–97.2) | 81.8 (23.9–97.2) | 81.8 (23.9–97.2) | 81.8 (23.9–97.2) |
| CFCS | 100 (—) | 100 (—) | 50 (0.6–91.1) | 50 (0.6–91.1) |
| Noonan‐like | 82.9 (47.2–95.5) | 73.7 (32.8–83.3) | 58.9 (32.8–83.3) | 39.3 (7–72) |
CFCS, cardiofaciocutaneous syndrome; CI, confidence interval; CS, Costello syndrome; NS, Noonan syndrome; NSML, Noonan syndrome with multiple lentigines.