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. 2024 Mar 29;103(13):e37625. doi: 10.1097/MD.0000000000037625

Table 1.

Dextrocardia/situs inversus totalis with spinal dysraphism in literature and our case.

Author, yr Age Gender Scoliosis type Complications
Davies et al, 1965[7] 32 Female Hemivertebrae Dextrocardia, rib deformities, mitral stenosis
Tubbs et al, 2003 11 Female Hemivertebrae Situs inversus totalis, Spina bifida occulta, type II split cord malformation, sacral lumbarization
Nallegowda et al, 2003[8] 12 Male Congenital scoliosis Situs inversus totalis, bilateral radial club hands, hypospadias, isolated dextrocardia, hypoplastic ribs, ectopic kidney, spina bifida occulta
Gul et al, 2006[4] Fetus Male Hemivertebrae Dextrocardia, polydactyl, atrial septal defect, hypoplastic ribs
Yu et al, 2009[5] 11 Male Congenital scoliosis Situs inversus totalis, type II split cord malformation, spina bifida occulta, hypoplastic ribs, coffee spots
Yu et al, 2009[5] 12 Female Hemivertebrae Situs inversus totalis, spina bifida occulta, coffee spots, abnormal hairs
Yu et al, 2009[5] 3 Male Hemivertebrae Situs inversus totalis, spina bifida occulta
María et al, 2014 14 Male Unknown Situs inversus totalis
Zhu et al, 2017[1] 9 Female Hemivertebrae Situs inversus totalis, syringomyelia, congenital heart defect, pulmonary dysfunction, hydronephrosis
Alkin et al, 2018 22 Female Unknown KS
Guo et al, 2022[9] 19 Male Idiopathic scoliosis KS, smell and hearing defects, Asthenoteratozoospermia
Guo et al, 2022[9] 37 Female Idiopathic scoliosis KS, smell and hearing defects, immature uterus
Our case, 2022 2 Female Hemivertebrae Situs inversus totalis, atrial septal defect, polydactyl

KS = Kartagener syndrome.