Table 1.
Dextrocardia/situs inversus totalis with spinal dysraphism in literature and our case.
| Author, yr | Age | Gender | Scoliosis type | Complications |
|---|---|---|---|---|
| Davies et al, 1965[7] | 32 | Female | Hemivertebrae | Dextrocardia, rib deformities, mitral stenosis |
| Tubbs et al, 2003 | 11 | Female | Hemivertebrae | Situs inversus totalis, Spina bifida occulta, type II split cord malformation, sacral lumbarization |
| Nallegowda et al, 2003[8] | 12 | Male | Congenital scoliosis | Situs inversus totalis, bilateral radial club hands, hypospadias, isolated dextrocardia, hypoplastic ribs, ectopic kidney, spina bifida occulta |
| Gul et al, 2006[4] | Fetus | Male | Hemivertebrae | Dextrocardia, polydactyl, atrial septal defect, hypoplastic ribs |
| Yu et al, 2009[5] | 11 | Male | Congenital scoliosis | Situs inversus totalis, type II split cord malformation, spina bifida occulta, hypoplastic ribs, coffee spots |
| Yu et al, 2009[5] | 12 | Female | Hemivertebrae | Situs inversus totalis, spina bifida occulta, coffee spots, abnormal hairs |
| Yu et al, 2009[5] | 3 | Male | Hemivertebrae | Situs inversus totalis, spina bifida occulta |
| María et al, 2014 | 14 | Male | Unknown | Situs inversus totalis |
| Zhu et al, 2017[1] | 9 | Female | Hemivertebrae | Situs inversus totalis, syringomyelia, congenital heart defect, pulmonary dysfunction, hydronephrosis |
| Alkin et al, 2018 | 22 | Female | Unknown | KS |
| Guo et al, 2022[9] | 19 | Male | Idiopathic scoliosis | KS, smell and hearing defects, Asthenoteratozoospermia |
| Guo et al, 2022[9] | 37 | Female | Idiopathic scoliosis | KS, smell and hearing defects, immature uterus |
| Our case, 2022 | 2 | Female | Hemivertebrae | Situs inversus totalis, atrial septal defect, polydactyl |
KS = Kartagener syndrome.