Figure 6: Copper enhances aggregational toxicity of mutant huntingtin.
Schematic model of synapse showing that under normal copper concentration, there is cytotoxicity of mutant Htt aggregates, and some co-localization of Ref(2)P with the aggregates. Under high Cu exposure, there is increased Ref(2)P clustering with Htt aggregates, increased cell death, and reduced BRP levels at the synapse. After Cu2+ chelation by DPA feeding, there is reduced Htt aggregates clustering.