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. 2024 Jan 23;25(3):1401. doi: 10.3390/ijms25031401

Table 1.

Updated Classification of Mastocytosis.

Cutaneous mastocytosis (CM)

  • Maculopapular cutaneous mastocytosis (MPCM)

  • ○

    Monomorphic variant

  • ○

    Polymorphic variant

  • Diffuse cutaneous mastocytosis (DCM)

  • Cutaneous Mastocytoma

Systemic mastocytosis (SM)
Non-advanced forms of SM

  • Indolent systemic mastocytosis (ISM)

  • Bone marrow mastocytosis (BMM)

  • Smoldering systemic mastocytosis (SSM)

Advanced forms of SM

  • SM with an associated hematologic neoplasm (SM-AHN)

  • Aggressive SM (ASM)

  • Mast cell leukemia (MCL)

Mast cell sarcoma (MCS)