Table 1.
The demographics and clinical characteristics of the patients at the time of diagnosis
| Characteristics | All patients N=40 |
| Age, years (median, range) | 51.5 (29–66) |
| Male, n (%) | 18 (45) |
| Time to diagnosis, months (median, range) | 25.4 (2.6–138.3) |
| Number of involved organs (median, range) | 6 (2–11) |
| Bone, n (%) | 40 (100) |
| Large vessels, n (%) | 32 (80) |
| Lung, n (%) | 28 (70) |
| Pleura, n (%) | 23 (58) |
| Retroperitoneum, n (%) | 22 (55) |
| Symptoms | N=40 |
| Cardiac symptoms, n (%) | 20 (50) |
| Palpitation | 4 (10) |
| Chest tightness | 11 (28) |
| Short of breath | 10 (30) |
| Oedema | 12 (30) |
| Extracardiac symptoms, n (%) | 30 (75) |
| Non-specific symptoms, n (%) | 14 (35) |
| Mutational status | N=32 |
| BRAFV600E, n (%) | 18 (56) |
| MAP2K1, n (%) | 3 (9) |
| Laboratory indexes | N=32 |
| hsCRP (mg/L, <3.0) | 20.9 (1.6–188.6) |
| ESR (mm/hour, <20.0) | 36.0 (3.0–103.0) |
ESR, erythrocyte sedimentation rate; hsCRP, hypersensitive C reactive protein.