Table 1.
Patient baseline characteristics.
| Features | n (%)/median (IQR) |
|---|---|
| Males | 18 (82%) |
| Age (years) | 73 (9) |
| Age at diagnosis (years) | 72 (10) |
| Weight (kg) | 69.5 (17.0) |
| BMI | 24.6 (5.4) |
| Duration of disease (years) | 1.6 (2.3) |
| Previous therapies | |
|
3 (13.6%) |
|
3 (13.6%) |
| Cardiac transplant | 2 (9.1%) |
| Perugini score* | |
|
12 (54,5%) |
|
7 (31.8%) |
| NIS score | 22 (23) |
| COMPASS-31 scale | 18 (30) |
| Norfolk quality of life | 36 (40) |
| Karnofsky performance status scale | 80 (10) |
| NYHA class | 2 (2) |
| Left ventricle wall thickness (mm) | 16.5 (4.9) |
| Left ventricle ejection fraction (%) | 53 (18) |
| Left ventricle telediastolic volume (mL) | 86 (40) |
| NT-ProBNP (pg/mL) | 1,300 (2795) |
*Available for 19 patients. NIS, Neuropathy Impairment Score; NYHA, New York Heart Association; NT-ProBNP, N-terminal pro–B-type natriuretic peptide.