Figure 3.

Performance of the ARVC Risk Score in DSP-TFC+ Patients

Performance of the ARVC risk calculator in DSP-TFC+ patients calibration plot for the performance of the ARVC risk calculator in the primary prevention cohort overall (A) and stratified on the presence (B) or absence (C) of left ventricular involvement. Average risk predicted by the ARVC risk calculator is plotted against the observed VA risk and associated 95% CI as estimated by the Kaplan-Meier method for each quintile (blue line). The linearity of this relationship is assessed using linear regression, and the coefficient of determination (r²) reflects the degree to which this relationship is appropriately characterized by a linear model. The red line reflects perfect, linear risk-prediction; risk predictions falling to the upper left of this line represent model underprediction, while risk prediction falling to the lower right of this line represent model overpredictions. ARVC = arrhythmogenic right ventricular cardiomyopathy; LV = left ventricular; VA = ventricular arrhythmias.