Table 2.
Demographics.
| Adults | Children | |
|---|---|---|
| No of individuals | 21 | 6 |
| Sex, n (%) | ||
| Male | 20 (95 %) | 6 (100 %) |
| Female | 1 (5 %) | 0 (0 %) |
| Age, Years | ||
| Mean (SD) | 36.1 (13.1) | 13.8 (1.83) |
| Range | 18–70 | 11–16 |
| Duration of LHON from onset, Years | ||
| Mean (SD) | 8.4 (6.0)a | 3.3 (2.7) |
| Range | 2–28 | 0.6–7 |
| Severity of visual impairment, n (%) | ||
| Some useful peripheral vision | 7 (33.3 %) | 2 (33.3 %) |
| Good peripheral vision | 4 (19 %) | 1 (16.7 %) |
| Light perception only (or shadows only) | 2 (9.5 %) | 0 (0 %) |
| I still have good overall vision | 1 (4.8 %) | 0 (0 %) |
| Good central vision | 1 (4.8 %) | 0 (0 %) |
| Moderate peripheral vision loss | 1 (4.8 %) | 2 (33.3 %) |
| Some useful central vision | 1 (4.8 %) | 1 (16.7 %) |
| Other | 4 (19 %) | 0 (0 %) |
| Treatment with idebenone, n (%) | 17 (80.9 %) | 6 (100 %) |
a
Duration of LHON was available only from 18 adult patients.