Table 3. Yamaguchi criteria.
Major criteria | Minor criteria | Exclusion criteria |
1. Fever more than equal to 39°C lasting for at least one week | 1. Sore throat | Infections, malignancy, other autoinflammatory disorders (mainly polyarteritis nodosa and rheumatoid vasculitis with extra-articular features) |
2. Enlargement of the lymph nodes | ||
2. Neutrophil predominant leukocytosis with WBC >10,000/mm3; polymorphs >80% | ||
3. Organomegaly-splenomegaly or hepatomegaly | ||
4. Deranged liver function tests | ||
3. Arthralgia or arthritis lasting for more than two weeks | ||
5. Negative ANA and rheumatoid factor tests | ||
4. Typical non-pruritic salmon pink skin rash |