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. 2024 May 3;183(8):3219–3232. doi: 10.1007/s00431-024-05579-3

Table 5.

Relationship between aortic root dilatation and other clinical features in children diagnosed with Marfan syndrome

n
mean ± SD
Aortic root dilatation
positive (n = 28)
Aortic root dilatation negative (n = 15) p
Male/female 32/11 21/7 11/4 0.904
Age (year) 12.56 ± 1.94 12.54 ± 5.43 10.8 ± 2.88 0.256
Height SDS 1.98 ± 0.56 1.60 ± 1.59 1.66 ± 1.46 0.908
FBN1 (+) 27 16 11 0.295
Ectopia lentis 16 9 7 0.347
Skeletal abnormalities 36 24 12 0.628
    Long limbs 36 24 12 0.628
    Thumb sign 27 16 11 0.295
    Wrist sign 23 13 10 0.204
    Pectus deformities 4 3 1 0.557
    Scoliosis 1 0 1 0.547
    Hindfoot 10 5 5 0.252
    Joint laxity 2 1 1 0.538
Facial abnormalities 19 13 6 0.685
    Long and narrow head 18 12 6 0.542
    High arched palate 7 6 1 0.352
    Malar hypoplasia 11 9 2 0.177
    Micor/retrognatia 10 6 4 0.258

The Student t test (two-sided), chi-square, and Fischer’s exact test were used; p < 0.05 is significant