Table 5.
Relationship between aortic root dilatation and other clinical features in children diagnosed with Marfan syndrome
n mean ± SD |
Aortic root dilatation positive (n = 28) |
Aortic root dilatation negative (n = 15) | p | |
---|---|---|---|---|
Male/female | 32/11 | 21/7 | 11/4 | 0.904 |
Age (year) | 12.56 ± 1.94 | 12.54 ± 5.43 | 10.8 ± 2.88 | 0.256 |
Height SDS | 1.98 ± 0.56 | 1.60 ± 1.59 | 1.66 ± 1.46 | 0.908 |
FBN1 (+) | 27 | 16 | 11 | 0.295 |
Ectopia lentis | 16 | 9 | 7 | 0.347 |
Skeletal abnormalities | 36 | 24 | 12 | 0.628 |
Long limbs | 36 | 24 | 12 | 0.628 |
Thumb sign | 27 | 16 | 11 | 0.295 |
Wrist sign | 23 | 13 | 10 | 0.204 |
Pectus deformities | 4 | 3 | 1 | 0.557 |
Scoliosis | 1 | 0 | 1 | 0.547 |
Hindfoot | 10 | 5 | 5 | 0.252 |
Joint laxity | 2 | 1 | 1 | 0.538 |
Facial abnormalities | 19 | 13 | 6 | 0.685 |
Long and narrow head | 18 | 12 | 6 | 0.542 |
High arched palate | 7 | 6 | 1 | 0.352 |
Malar hypoplasia | 11 | 9 | 2 | 0.177 |
Micor/retrognatia | 10 | 6 | 4 | 0.258 |
The Student t test (two-sided), chi-square, and Fischer’s exact test were used; p < 0.05 is significant