Table 1.
Baseline Clinical Characteristics of Interrupted IVC Patients Undergoing Fontan Completion or Fontan Revision
| Prospective Patients |
||||
|---|---|---|---|---|
| P1 | P2 | P3 | P4 | |
| Diagnosis | Heterotaxy (polysplenia), dextrocardia, {A,L,L} DORV, RdAVC, iIVC bilateral SVC | Heterotaxy (polysplenia) with CAVC, iIVC with azygos continuation to LSVC, bilateral SVC | Heterotaxy with {A,D,D} DORV with LdAVC, iIVC with azygos continuation | Heterotaxy, {A,D,D} TGA/VSD, bilateral SVC, iIVC with azygos continuation to LSVC |
| Age (y) | 4.0 | 9.3 | 18.0 | 13.4 |
| BSA (m2) | 0.63 | 0.98 | 1.75 | 1.16 |
| SVC anatomy | Bilateral | Bilateral | Single LSVC | Bilateral |
| Surgical stage | Bilateral BDG-Kawashima | Fontan completion | Fontan completion | Fontan completion |
| AVM presence | No evidence | Left lung | Left lung | Left lung |
| AVM grade | None | Macro | Micro | Micro |
| Baseline O2 saturation (%) | 88 | 86 | 91 | 91 |
| Left pulmonary vein O2 saturation (%) | 97 | 68 | 86 | 83 |
| PA pressures (mm Hg) | 11 | 17 | 16 | 18 |