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. 2024 Aug 26;14:19748. doi: 10.1038/s41598-024-70642-w

Table 2.

Genes of interest selected after manual annotation, together with their RNA-seq, PCR and genomic validations, predictions of effects in humans following the SIFT and Poly-Phen models, and Clinvar accession number of information related to the residue position.

Gene Variant Species RNA-seq validation Genomic validation PCR validation SIFT PolyPhen Clinvar accession2
ACE R508H Hatl Yes (50%) Yes (50%) yes T (0.57) PsD (0.757)
ATM R184Q Hmed yes yes yes APF (0.00) PbD (0.992) VCV000481315.7
ATM Q2177R Hmed yes yes yes APF (0.00) PbD (0.999) VCV001810514.4
ATM L8F Hatl yes yes yes APF (0.03) PbD (1.00) VCV000487013.7
ATM V1085I Hatl yes yes yes APF (0.01) PbD (0.995) VCV000453455.2
ATM I2914V Hatl yes yes yes APF (0.03) B (0.208) VCV000187320.22
ATM V2937M Hatl yes yes yes APF (0.01) PsD (0.929) VCV000187681.3
BLM M827V1 Hatl yes yes yes T (0.10) PbD (1.00)
BLM I1039V1 Hatl yes yes yes T (0.11) B (0.004)
BRCA2 S2807R Hmed yes yes yes APF (0.00) PbD (0.982) VCV000216033.5
BRCA2 S2807C Hatl yes yes yes APF (0.00) PsD (0.461) VCV000441481.16
CETP V29A Hmed no reads yes yes APF (0.02) B (0.001)
DOCK8 R398H Hmed yes yes yes APF (0.00) PbD (0.999) VCV000235481.7
FANCA M427V Hatl yes yes B (0.271) VCV001023721.1
FANCI S979T Hmed yes yes yes B (0.230) VCV000408250.1
NUDT1 G99S Hmed yes yes yes APF (0.00) PsD (0.772)
SIRT1 V412I Hatl yes yes yes APF (0.03) PsD (0.925)
XRCC5 E417Q Hatl yes yes yes T (0.29) PsD (0.770)
XRCC5 M427T Hatl yes yes yes APF (0.00) B (0.128)

B: Benign; PbD: Probably damaging; PsD: Possibly damaging; T: Tolerated; APF: Affect protein function. Hmed: H. mediterraneus, Hatl: H. atlanticus.

1Note that in Drosophila melanogaster variants are M827I and I1039A.

2Only one Clinvar accession number is shown, even if there was more than one for each position.