3-TYP	3-(1H-1,2,3-triazol-4-yl) pyridine
α-LA	alpha-lipoic acid
α-KGDH	alpha-ketoglutarate dehydrogenase
AceCS2	acetyl-CoA synthetase 2
ACP	acyl carrier protein
ACSM2A	acyl-CoA synthethase medium-chain family member 2A
AMP	adenosin monophosphate
AMPK	AMP-activated protein kinase
ASCL1	achaete-scute family BHLH transcription factor 1
ATF4	activating transcription factor 4
ATF5	activating transcription factor 5
ATP5F1A	ATP synthase F1 subunit 1 alpha
BCKDH	branched chain ketoacid dehydrogenase
BRN2	POU class 3 homeobox 2
BSA	bovine serum albumin
CoA	coenzyme A
CoPAN	CoA synthase protein-associated neurodegeneration
COX IV	cytochrome C oxidase subunit IV
CPI-613	6,8-bis (benzylthiol)-octanoic acid
DAPI	4′,6-diamidino-2-phenylindole
DMEM	Dulbecco’s modified Eagle medium
DMSO	dimethyl sulfoxide
FAO	fatty acid oxidation
mtFASII	mitochondrial fatty acid synthesis type II
FBS	fetal bovine serum
FCCP	carbonyl cyanide 4-(trifluoromethoxy) phenylhydrazone
FOXO3A	forkhead box O3
GCS	glycine cleavage system
GCSH	glycine cleavage system H protein
H2AX	H2A histone family member X
HEPES	4-(2-hydroxyethyl)-1-piperazine ethanesulfonic acid
HRP	horseradish peroxidase
Hsp60	heat shock protein 60
Hsp70	heat shock protein 70
IC50	half-maximal inhibitory concentration
ICP-MS	inductively coupled plasma mass spectrometry
IDO1	indoleamine 2,3-dioxygenase 1
IEM	inborn error of metabolism
iNs	induced neurons
ISC	iron sulfur cluster
LIAS	lipoic acid synthase
lip3	lipoate-protein ligase 3
LIPT1	lipoyltransferase 1
LIPT1	lipoyltransferase 1
LIPT2	lipoyl (octanoyl) transferase 2
Lonp1	lon peptidase 1
LplA	lipoate-protein ligase A
MetAP2	methionine aminopeptidase 2
MePAN	mitochondrial enoyl CoA reductase protein-associated neurodegeneration
MnSOD	manganese superoxide dismutase
MRI	magnetic resonance imaging
mt-CO2	mitochondrially encoded cytochrome C oxidase subunit II
mtDNA	mitochondrial DNA
mtETC	mitochondrial electron transport chain
mtUPR	mitochondrial unfolded protein response
NAD+	nicotinamide adenine dinucleotide
NAMPT	nicotinamide phosphoribosyltransferase
NBIA	neurodegeneration with brain iron accumulation
nDNA	nuclear DNA
NDUFA9	NADH:ubiquinone oxidoreductase subunit A9
Nrf1	nuclear respiratory factor 1
Nrf2	nuclear respiratory factor 2
OADH	2-oxoadipate dehydrogenase
OCR	oxygen consumption rate
OXPHOS	oxidative phosphorylation
PBS	phosphate-buffered saline
PDH	pyruvate dehydrogenase
PFA	paraformaldehyde
PGC-1α	peroxisome proliferator-activated receptor-γ coactivator 1-α
P-PGC-1α	phosphorylated peroxisome proliferator-activated receptor-γ coactivator 1α
PGK	phosphoglycerate kinase
PKAN	pantothenate kinase-associated neurodegeneration
ROS	reactive oxygen species
SIRT1	sirtuin 1
SIRT3	sirtuin 3
TCA	tricarboxylic acid
TEM	transmission electron microscope
TOMM20	translocase of the outer mitochondrial membrane 20
TFAM	mitochondrial transcription factor A
UQCRC1	ubiquinol cytochrome C reductase core protein 1
VDAC1	voltage-dependent anion channel 1