Table 2.
Comparison of the prevalence of primary cutaneous lymphomas between subgroups according to the year of diagnosis.
Relative frequency of primary cutaneous lymphomas (n, %) | ||||
---|---|---|---|---|
1994–2003 | 2004–2013 | 2014–2022 | Overall | |
Cutaneous mature T-and NK-cell lymphomas (CTCL) | n = 86 | n = 186 | n = 275 | n = 547 |
Mycosis fungoides | 23 (26.7) | 64 (34.4) | 152 (55.3) | 239 (43.7) |
Sézary syndrome | 1 (1.2) | 3 (1.6) | 0 (0.0) | 4 (0.7) |
Primary cutaneous anaplastic large cell lymphoma | 12 (14.0) | 36 (19.4) | 25 (9.1) | 73 (13.3) |
Lymphomatoid papulosis | 22 (25.6) | 37 (19.9) | 39 (14.2) | 98 (17.9) |
Primary cutaneous extranodal NK/T-cell lymphoma | 8 (9.3) | 16 (8.6) | 11 (4.0) | 35 (6.4) |
Subcutaneous panniculitis-like T-cell lymphoma | 8 (9.3) | 13 (7.0) | 17 (6.2) | 38 (6.9) |
Primary cutaneous CD4-positive small/medium T-cell lymphoproliferative disorder | 1 (1.2) | 2 (1.1) | 19 (6.9) | 22 (4.0) |
Primary cutaneous peripheral T-cell lymphoma, NOS | 11 (12.8) | 15 (8.1) | 12 (4.4) | 38 (6.9) |
Cutaneous Mature B-cell lymphomas (CBCL) | n = 9 | n = 32 | n = 39 | n = 80 |
Primary cutaneous marginal zone lymphoma | 5 (55.6) | 22 (68.8) | 23 (59.0) | 50 (63.3) |
Primary cutaneous diffuse large B-cell lymphoma, leg typer | 4 (44.4) | 9 (28.1) | 13 (33.3) | 26 (32.9) |
Primary cutaneous follicle center lymphoma | 0 (0) | 1 (3.1) | 2 (5.1) | 3 (3.8) |
EBV-positive mucocutaneous ulcer | 0 (0) | 0 (0) | 1 (2.6) | 1 (1.3) |
CTCL/CBCL ratio | 9.6:1 | 5.8:1 | 7.1:1 | 6.8:1 |