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. 2024 Aug 20;15:1460320. doi: 10.3389/fendo.2024.1460320

Table 3.

Management of hypertensive crises induced by catecholamine secreting tumors in children (8, 10, 11, 14).

Drug Mechanism Dosage Side effects Contraindications
FIRST LINE TREATMENT
Urapidil Selective α1-adrenergic receptor antagonist - central serotoninergic 1A receptor agonist Initial 0.5–4.0 mg/kg per hour Maintenance 0.2–2.0 mg/kg per hour Hypotension, tachycardia, dizziness, central sedation, nausea and nasal congestion Athero-venous shunt, stenosis of the aortic isthmus
Phentolamine Competitive non selective α1/α2 adrenergic receptor antagonist Bolus 0.1-5 mg/Kg Hypotension, tachycardia, dizziness, central sedation, arrythmias and nasal congestion //
Labetalol (in case of concomitant tachyarrhythmias, after adequate α-adrenergic blockade) Combinate α1/β-adrenergic blocker (ratio 1:7) 0.25–3 mg/kg/hour Titrate slowly Max: 3 mg/kg/hour Orthostatic hypotension, dizziness Asma, sinuses bradycardia, atrio-ventricular block, heart failure
Esmolol (in case of concomitant tachyarrhythmias, after adequate α-adrenergic blockade) Selective β1-adrenergic blocker Bolus of 500–600 μg/kg over 2 min. Maintenance 200 (50–250) μg/kg/min. Max 500 µg/Kg/min Hypotension, bradycardia, risk of atrio-ventricular block Asma, sinuses bradycardia, sick sinus syndrome, atrio-ventricular block, hypotension, heart failure, cardiogenic shock, pulmonary hypertension
SECOND LINE TREATMENT
Sodium nitroprusside Vasodilator (nitro-derivates) Starting: 0.3–0.5 µg/kg/min. Titrate by 0.1 µg/kg/min every few minutes. Max: 10 µg/kg/min Tachycardia, flushing, palpitations, and hypotension. Monitor for risk of cyanide and
thiocyanate toxicity (so protect from light)
Renal and/or hepatic failure, hypothyroidism, deficit of vitamin B12
Nicardipine Dihydropyridine calcium channel blocker Starting: 0.5–1 µg/kg/min. Max: 4–5 µg/kg/min Tachycardia, flushing, palpitations, and hypotension, edema, headache Pathological hyperlipemia, nephrosis or acute pancreatic inflammation secondary to hyperlipemia
OTHER TREATMENTS
Magnesium sulphate Vasodilator, inhibits catecholamine release from adrenal medulla and sympathetic paraganglia Loading dose: 40–60 mg/kg over 10 minutes. Maintenance: 15–30 mg/kg/hour Neuromuscular paralysis Use with caution in those with neuromuscular disease (risk of paralysis)
Dexmedetomidine Central α2-agonist Loading dose: 0.5–1 µg/kg/dose over 10 minutes. Maintenance: 0.2–0.5 µg/kg/hour Respiratory depression, bradycardia, xerostomia In those with reduced respiratory drive