Table 1.

A) Baseline Laboratory Values of Individuals with WNT2B Deficiency
	Aldosterone	Renin	ARR	BUN	Creatinine
Individual A	583	286.5	2.0	3.2	39
Individual B	323	341.1	0.9	4.5	23
Reference	140–2220 pM	5.4–34.5 ng/dL	10.2–23.7 pM/ng	2–8 mM	17.7–79.6
Individual C	12	18	0.67	12	0.2
Reference	7–54 ng/dL	1.7–11.2 ng/mL/h	0.80–13.10	15–18 mg/dL	0.2–0.4 mg/dL

B) Response to Fludrocortisone (Individual C)
Age (Months)	25	30	31	32	37
Fludrocortisone	0 mg	0.1 mg	0.05 mg	0.05 mg	0.05 mg
						Reference
Aldosterone	8.5	<1.0	<1.0	<1.0	<1.0	7–54 ng/dL
Renin	19.0	0.76	1.0	9.6	8.6	1.7–11.2 ng/mL/h
ARR	0.67	0.45	--	--	--	0.80–13.10