Figure 8.

Desmoplakin-Related Arrhythmogenic Cardiomyopathy

(A) A 12-lead electrocardiogram showing low QRS voltages in limb leads and diphasic T-waves in the lateral leads. (B) Short-axis T2-weighted CMR image showing myocardial edema in the lateral wall. Short-axis (B) and 4-chamber (D) CMR images showing extensive late gadolinium enhancement as a stria proceeding from epicardium toward endocardium in the lateral wall with partial apical involvement. (C) Two-dimensional echocardiography speckle tracking analysis highlighting concordant regional impairment. CMR = cardiac magnetic resonance.