Table 1.
Demographics and Clinical Characteristics
| Category | No. (%) | Age at first visit, median (IQR), y | Age at disease onset, median (IQR), y | Median age at death, median (IQR), y |
|---|---|---|---|---|
| Overall | 1442 (100.0) | 64.8 (57-72) | 63.4 (56-70) | 66.6 (59-73) |
| Sex/site of onset | ||||
| Female | ||||
| Bulbar | 252 (17.5) | 66.7 (61-74) | 65.6 (60-73) | 68.9 (63-75) |
| Spinal | 419 (29.1) | 64.4 (56-72) | 63.2 (55-70) | 66.0 (58-70) |
| Total | 671 (46.5) | 65.6 (58-72) | 64.5 (57-71) | 67.8 (60-74) |
| Male | ||||
| Bulbar | 183 (12.7) | 65.8 (59-72) | 65.1 (57-71) | 67.8 (61-73) |
| Spinal | 588 (40.8) | 62.9 (54-71) | 61.5 (53-69) | 64.8 (57-69) |
| Total | 771 (53.5) | 63.7 (55-71) | 62.3 (54-70) | 65.6 (57-73) |
| Ethnoracial | ||||
| Non-Hispanic White | 1,327 (92.0) | 65.1 (57-72) | 63.2 (55-70) | 66.3 (58-73) |
| African American | 80 (5.5) | 59.8 (51-68) | 67.6 (62-74) | 71.8 (66-80) |
| Hispanic | 28 (1.9) | 61.8 (59-67) | 70.9 (63-80) | 73.4 (65-82) |
| Asian | 5 (0.3) | 64.2 (54-72) | 67.0 (59-73) | 68.4 (62-74) |
| Other | 2 (0.1) | 66.7 (49-84) | 70.8 (68-74) | 70.8 (68-74) |
Abbreviation: IQR, interquartile range.