Table 1.
Characteristic | Number |
---|---|
Total patients | 240 |
Sex | |
Female | 81 (34%) |
Male | 159 (66%) |
Age at initial visit (years), mean ± SD | 71 ± 8.8 |
Follow-up period (days), mean ± SD | 382 ± 281 |
Smoking history (BI > 100) | 139 (58%) |
ILD pattern | |
UIP | 65 (27%) |
Possible UIP | 48 (20%) |
Inconsistent with UIP | 80 (33%) |
Diffuse alveolar damage | 7 (3%) |
Organizing pneumonia | 40 (17%) |
Outcome | |
Acute exacerbation | 27 (11%) |
Death | 32 (13%) |
Treatment | |
Corticosteroids | 96 (40%) |
Immunosuppressant drugs | 15 (6%) |
Anti-fibrotic drugs | 20 (8%) |
MSA profile | |
PL-7 | 16 (6.7%) |
SRP | 13 (5.4%) |
PL-12 | 9 (3.8%) |
Mi-2 | 8 (3.3%) |
OJ | 7 (2.9%) |
EJ | 3 (1.3%) |
Jo-1 | 1 (0.4%) |
BI, Brinkman Index; ILD, interstitial lung disease; MSA, myositis-specific antibodies; SD, standard deviation; UIP, usual interstitial pneumonia