Table 1.

Diagnosis criteria in different clinical aspects of the fibrillinopathy [6].

Disease Type	Z Score	SS	Ectopia Lentis
MS	≥3 (children)/≥2 (adults)	-	Yes
MS	≥3 (children)/≥2 (adults)	≥7	No
MASS	<3 (children)/<2 (adults)	≤5	No
MVPS	<3 (children)/<2 (adults)	<5	No