Table 1.

Cases by primary neuropathological diagnosis

Diagnosis	Total	Birth sex			Age at death				Biondi bodies
		Female	Male	N/A	Mean	Min	Max	N/A	+	−
Alzheimer disease, Dominantly Inherited	27	14	13	0	51.2	34	76	1	15	12
Alzheimer disease, Sporadic	439	238	198	3	77.4	40	103	3	423	16
Diffuse Lewy body disease	139	41	98	0	78.5	58	95	0	137	2
Multiple system atrophy	6	4	2	0	71.5	52	83	0	6	0
FTLD-Tau, Hereditary	18	9	9	0	58.2	47	65	0	14	4
FTLD-Tau, Sporadic	78	34	44	0	72.3	49	94	0	74	4
FTLD-TDP-43, Hereditary	38	16	22	0	64.3	42	81	0	35	3
FTLD-TDP-43, Sporadic	23	9	14	0	68.1	50	92	0	20	3
Creutzfeldt-Jakob disease, Hereditary	9	5	4	0	61.7	42	85	0	7	2
Creutzfeldt-Jakob disease, Sporadic	115	65	50	0	65.3	33	91	0	93	22
Gerstmann-Sträussler-Scheinker disease	30	12	17	1	53.9	38	73	1	15	15
Amyotrophic lateral sclerosis	14	4	10	0	64.6	49	77	0	14	0
Cerebrovascular disease	27	9	18	0	80.3	52	98	0	26	1
Miscellaneous	29	11	18	0	55.5	5	85	1	18	11
To be determined	134	45	74	15	66.3	14	96	18	108	26
TOTAL	1126	516	591	19	71.73	5	103	24	1005	121

Frontotemporal Lobar Degeneration (FTLD), TAR DNA-binding protein 43 (TDP-43), Positive ( +), Negative (−)