Table 1.
Subject characteristics, exercise capacity and muscle strength
| Subject 1 | Subject 2 | Control subjects Mean (SD) | |
| Age (years) | 10.2 | 8.7 | 12.6 (2.6) |
| Weight (kg) | 33 (SD-score 0) | 25 (SD-score -1) | 42.6 (6.5) (SD-score 0.01) |
| Height (cm) | 143 (SD-score 0) | 133 (SD-score 0) | 154.6 (10.6) (SD-score -0.4) |
| Wpeak (Watt) | 115 | 70 | 145 (70) |
| HRpeak (b·min-1) | 195 | 195 | 185 (5) |
| RERpeak | 1.27 | 1.25 | 1.22 (0.11) |
| VO2peak (L·min-1) | 1.4 (SD-score -1.5) | 1.2 (SD-score -1) | 1.5 (0.46) (SD-score -1.6) |
| VO2peak (ml·kg-1·min-1) | 42.8 (SD-score -1.65) | 50.2 (SD-score 0.06) | 35.3 (5.3) (SD-score -2.17) |
| Peak blood lactate 3 min after the exercise test (mmol·l-1) | 7.3 | 6.0 | 6.5 (3.6) |
| Quadriceps muscle strength (N) | 207 (SD-score 0.2) | 156 (SD-score 0.8) | NM |
Abbreviations: Wpeak: peak workload, HRpeak: peak heart rate, RERpeak: peak Respiratory Exchange Ratio, VO2peak: peak oxygen uptake, SD-score: standard deviation score, NM: not measured.