Table 2.  Physical function evaluation data.
Physical function | All patients (n=26) | SMA type 3 (n=15) | SMA type 2 (n=11) | P value |
6MWT, m | 0 [91] | 74.5 [307.8] | 0 [0] | 0.009 |
HFMSE | 15 [48.0] | 46 [37.5] | 3 [3.5] | 0.01 |
RULM | 11.5 [26] | 30 [19.5] | 4 [2] | 0.01 |
Right grip, N | 7.8 [16.2] | 18.6 [67.8] | 3.9 [4.9] | 0.012 |
Left grip, N | 10.8 [20.6] | 22.5 [43.6] | 3.9 [8.8] | 0.011 |
Right Palmar pinch, N | 2.9 [5.9] | 6.8 [18] | 1.9 [2.0] | 0.015 |
Left Palmar pinch, N | 3.4 [5.35] | 6.3 [14.2] | 1.9 [1.5] | 0.01 |
Right Key pinch, N | 5.8 [11.3] | 13.2 [43.3] | 1.9 [3.7] | 0.01 |
Left Key pinch, N | 4.9 [7.9] | 7.7 [30.1] | 1.9 [2.5] | 0.011 |
Normalized right grip, N/kg | 0.34 [0.81] | 0.93 [1.50] | 0.20 [0.23] | 0.006 |
Normalized left grip, N/kg | 0.32 [0.62] | 0.79 [1.52] | 0.22 [0.20] | 0.01 |
Normalized right Palmar pinch, N/kg | 0.15 [0.31] | 0.27 [0.36] | 0.07 [0.09] | 0.05 |
Normalized left Palmar pinch, N/kg | 0.13 [0.28] | 0.32 [0.31] | 0.07 [0.08] | 0.011 |
Normalized right Key pinch, N/kg | 0.22 [0.77] | 0.62 [0.88] | 0.12 [0.15] | 0.011 |
Normalized left Key pinch, N/kg | 0.16 [0.42] | 0.41 [0.46] | 0.07 [0.09] | 0.016 |
Data given as median [IQR]. Maximum possible scores: HFMSE, 66; RULM, 37. Normalized data are relative to body weight.