Table 1.

Modified Zajicek criteria for the diagnosis of neurosarcoidosis

Definitive	Clinical presentation suggestive of neurosarcoidosis with exclusion of differential diagnoses and histologic confirmation of nervous system involvement
Probable	Clinical presentation suggestive of neurosarcoidosis with evidence of CNS inflammation (elevated levels of CSF protein and/or cells, the presence of oligoclonal bands and/or MRI evidence compatible with neurosarcoidosis) and exclusion of differential diagnoses together with evidence for systemic sarcoidosis (positive histology and/or at least two indirect indicators as fluorodeoxyglucose positron emission tomography (FDG-PET), gallium scan, high-resolution chest computed tomography, bronchoalveolar lavage (BAL))
Possible	Clinical presentation suggestive of neurosarcoidosis with exclusion of differential diagnoses where the above-mentioned criteria are not met