Table 1. Classification of phakomatosis pigmentovascularis.

Type [according to Happle (4)]	Type [according to Hasegawa and Yasuhara (2)]	Vascular lesion	Pigmentary lesion
Excluded nevus	I	Nevus flammeus	Verrucous and pigmented
Cesiofammea	II	Nevus flammeus ± anemic nevus	Mongolian spot
Spilorosea	III	Nevus flammeus ± anemic nevus	Nevus spilus
Non-classifiable	IV	Nevus flammeus ± anemic nevus	Mongolian spot, nevus spilus
Cesiomarmorata	V	Cutis marmorata telangiectatica congenita	Mongolian spot

This table was adapted from an Open Access article (5) under the terms of the Creative Commons Attribution Non-Commercial License.